Glycosade — Advanced Slow-Release Starch for Liver Glycogen Storage Disease (GSD)

Glycosade is a patented, hydrothermally processed high-amylopectin cornstarch powder designed specifically for the dietary management of hepatic glycogen storage diseases (GSD) in children and adults. It offers a longer-lasting source of carbohydrate to help maintain safe blood glucose levels between meals or overnight, giving patients greater freedom and less frequent dosing.

Why Glycosade® Stands Out

• Slow-release performance: Its unique processing gives a more gradual glucose-release profile versus standard uncooked cornstarch (UCCS), allowing longer periods of stable blood sugar and less frequent dosing, especially overnight.
• Specialised for GSD: Indicated for hepatic GSD types (e.g., GSD Ia, Ib, 0, III, VI, IX) where a long-acting starch is needed to reduce hypoglycemia risk and improve metabolic control.
• Flexible use options: Available in unflavoured and lemon flavours. Suitable for oral drinking, mixing into foods, or bolus tube feeding under medical supervision.
• Formula details: Each 60 g sachet (typical dose) provides about 212 kcal and 53 g of carbohydrate; 0 g protein and 0 g sugar.

How to Use

• Preparation: Add the recommended dose (e.g., one 60 g sachet) to ~100 mL cold water or mix into chilled yoghurt/soft food. Do not heat, as heating alters its release profile.
• For tube feeding: Dilute appropriately and administer as a bolus feed via feeding tube, flushing before and after.
• Dosage: Dosing is highly individual — based on age, GSD type, weight, metabolic needs, and clinical monitoring. Must be initiated and managed under the supervision of a metabolic specialist or dietitian.

Important Things to Know

• Glycosade is a food for special medical purposes, not for general use. It must be used only under the guidance of a doctor, dietitian and nurse experienced in GSD.
• Not intended to be the sole nutrition source; other dietary foods, fluids, and monitoring remain essential.
• Because its effect is slower-acting, care must be taken during transitions or illness — blood glucose/lactate monitoring is critical especially when first switching from standard cornstarch or starting Glycosade® for the first time.
• Available for use in children (from 2-5 yrs, depending on region) and adults; suitability must be determined by a metabolic team.